Title

Examination Of The Cognitive Profile Of Adults With Prader-Willi Syndrome Using The Dementia Rating Scale-2: A Pilot Study

Keywords

adults with intellectual disability; cognitive abilities; Dementia Rating Scale; neuropsychological testing; Prader-Willi syndrome

Abstract

Background The goal of the current study was to determine if the Dementia Rating Scale-2 (DRS-2) is an appropriate tool for evaluating cognitive abilities in adults with Prader-Willi syndrome (PWS). The DRS-2 is a screening measure previously utilised in low-functioning populations with and without dementia, including individuals with intellectual disability.Method Thirteen adults with PWS between 21 and 59 years old were administered the DRS-2.Results Participants demonstrated impairment on all 5 subscales, with the largest impairments observed on the Initiation/Perseveration and Construction subscales. No significant floor or ceiling effects were observed. No correlations were observed between age and any subscale score.Conclusion The DRS-2 may be a valid assessment tool for capturing the full spectrum of cognitive functioning in adults with PWS. The largest impairments were observed on items requiring verbal and motor fluency and visuo-spatial processing. Future directions for the use of the DRS-2 in this population are discussed. © 2013 Australasian Society for Intellectual Disability, Inc.

Publication Date

1-2-2014

Publication Title

Journal of Intellectual and Developmental Disability

Volume

39

Issue

1

Number of Pages

102-107

Document Type

Article

Personal Identifier

scopus

DOI Link

https://doi.org/10.3109/13668250.2013.870330

Socpus ID

84893963951 (Scopus)

Source API URL

https://api.elsevier.com/content/abstract/scopus_id/84893963951

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