Title

Colorectal Cancer in a Monoallelic MYH Mutation Carrier

Authors

Authors

R. Khalaf; C. Jones; W. Strutt;P. Williamson

Comments

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Abbreviated Journal Title

J. Gastrointest. Surg.

Keywords

Colorectal cancer; MYH polyposis; Monoallelic mutations; Biallelic; mutations; POLYPOSIS; Gastroenterology & Hepatology; Surgery

Abstract

Although the literature describes mutY homolog gene (MYH) polyposis as an autosomal recessive syndrome, we report a case of colorectal cancer in a carrier of MYH polyposis. Biallelic mutations in the MYH gene have been shown to increase the risk of colorectal cancer over the lifetime of the mutation carrier.1,2 However, there is no clear consensus in the literature as whether a monoallelic mutation increases the risk for colorectal cancer.3 In this report, we postulate that a single mutation is sufficient to increase the risk of colorectal cancer. We also propose that the G382D MYH mutation may play a dominant rather than a recessive role in polyposis and cancer development.

Journal Title

Journal of Gastrointestinal Surgery

Volume

17

Issue/Number

8

Publication Date

1-1-2013

Document Type

Article

Language

English

First Page

1500

Last Page

1502

WOS Identifier

WOS:000321837900022

ISSN

1091-255X

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